Reni Ghrahani Departemen of Child Health Faculty of Medicine Universitas Padjadjaran, Bandung, Indonesia E-mail: email@example.com
Vasculitis is a rare condition in children, defined as the presence of inflammation in a blood vessel.1-3 Vasculitis can be classified based on clinical phenotypes (organ-specific vs. systemic), underlying causes (primary or secondary disease), histological patterns (granulomatous or non-granulomatous), and primarily affected vessel sizes (based on Chapel Hill and EULAR/PRES classifications) as presented in table 1 and 2.2, 4 This paper provides a classification of childhood vasculitis, focusing on primary systemic vasculitis, as well as the clinical presentation and diagnostic evaluation for the most common vasculitides. The annual incidence of primary vasculitis in children and adolescents is approximately 23 per 100,000 in UK. Primary vasculitis accounts for approximately 2?10% of all pediatric conditions evaluated in pediatric rheumatology clinics.1 There was no incidence data in Indonesia yet. Henoch Sch
1. Weiss PF. Pediatric vasculitis. Pediatric clinics of North America. 2012;59(2):407-23. 2. Schnabel A, Hedrich CM. Childhood Vasculitis. 2019;6(421). 3. Basak R, Ganguli S, Rapaport S. Pediatric vasculitis. 2014;15(2):61-5. 4. Ozen S, Ruperto N, Dillon MJ, Bagga A, Barron K, Davin JC, et al. EULAR/PReS endorsed consensus criteria for the classification of childhood vasculitides. Annals of the rheumatic diseases. 2006;65(7):936-41. 5. Khubchandani RP, Viswanathan V. Pediatric Vasculitides: A Generalists Approach. Indian J Pediatr. 2010;77:1165-71. 6. Okazaki T, Shinagawa S, Mikage H. Vasculitis syndrome-diagnosis and therapy. Journal of general and family medicine. 2017;18(2):72-8. 7. Khanna G, Sargar K, Baszis KW. Pediatric Vasculitis: Recognizing Multisystemic Manifestations at Body Imaging. 2015;35(3):849-65.